Ohvira Syndrome, about a case
DOI:
https://doi.org/10.47606/ACVEN/MV0231%20Keywords:
Ohvira, vaginal atresia, Renal anomaly, VaginoplastyAbstract
Introduction: OHVIRA syndrome is a congenital malformation characterized by didelphys uterus, total or partial blind hemivagina and ipsilateral renal anomaly. The association of these three components is secondary to an anomaly in embryological development caused by the proximity of the structures derived from the mesonephric primordium (Wolf's duct) and the paramesonephric primordium (Müllerian duct). Objective: Describe a clinical case of a patient who meets the criteria for Ohvira syndrome. Case report A 12-year-old patient with a surgical history of laparoscopy with findings of hematocolpos, right ovarian hemorrhagic cyst, left hydrosalpinx and vaginal septum. Results: It is estimated that the incidence of this syndrome is unknown, but it corresponds to between 0.1-3.5% of all Müllerian malformations. Conclusions: Once Ohvira syndrome is diagnosed with the radiological findings of a bicornuate uterus, right kidney anomaly, and surgical findings of partial vaginal atresia, it is necessary to establish the clinical-surgical evolution to avoid gynecological-obstetric and surgical complications, such as infertility, abortions, dysfunction of the plasty, among others.
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Copyright (c) 2024 María Elizabeth Bravo Bazurto, María Yuliana Díaz Garay, Verónica Ayling Lama Asinc, Viviana Gissela Olmedo Becerra, Edison Esteban Terán Pazmiño, Andrea Jeanette Vélez Vera
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